Korean J Urol.
2013 Mar;54(3):209-211.
Immunoglobulin G4-Related Systemic Sclerosing Disease: A Case Involving the Ureter and Kidney
- Affiliations
-
- 1Department of Urology, Kyung Hee University Hospital at Gangdong, Seoul, Korea. yookoohan@yahoo.co.kr
Abstract
- Immunoglobulin (Ig) G4-related sclerosing disease is a newly defined clinicopathological entity characterized by lymphoplasmacytic infiltration of IgG4-positive plasma cells and varying degrees of fibrosis within affected tissues. Patients usually exhibit multisystem involvement and often respond well to steroid and immunosuppressive therapy. This report presents a case of IgG4-related sclerosing disease involving the ureter and kidney. We hope to bring IgG4-related sclerosing disease to the attention of urologists, because it is an uncommon disease that commonly responds to systemic corticosteroids.