J Korean Assoc Oral Maxillofac Surg.  2018 Apr;44(2):86-90. 10.5125/jkaoms.2018.44.2.86.

Modified two flap palatoplasty in asymptomatic transsphenoidal encephalocele: a case report

• Richardson S
• Khandeparker RV
• Raghuvaram AK
• Mohan R

• KMID: 2410585
• DOI: http://doi.org/10.5125/jkaoms.2018.44.2.86

Abstract

About one-third of patients with transsphenoidal basal encephaloceles have associated congenital anomalies, including cleft palate. Moreover, they are often plagued by symptomatic exacerbations in the form of upper respiratory obstructions, cerebrospinal fluid leaks, meningitis, etc., with few patients being asymptomatic. We herein present a rare asymptomatic case of transsphenoidal basal encephalocele in an 18-month-old child with cleft palate and highlight a modified version of two-flap palatoplasty.

Keyword

Basal encephalocele; Transsphenoidal variant; Asymptomatic; Cleft palate; Palatoplasty

MeSH Terms

Cerebrospinal Fluid Leak
Child
Cleft Palate
Encephalocele*
Humans
Infant
Meningitis

Figure

• 

  Fig. 1 Preoperative clinical photographs and computed tomography (CT) scan of the patient. A. Extraoral photograph. B. Intraoral photograph. C, D. Axial and coronal CT views showing the opening in the sphenoid bone, as well as herniation of the mass in the palate (arrows).

• 

  Fig. 2 Intraoperative photographs of the patient. A. Palatal mucoperiosteal flaps raised. B. Deepithelialization of the encephalocele. C. Closure of the mucoperiosteal flaps over the encephalocele.

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  Fig. 3 Postoperative photographs of the patient at 3 years follow-up. A. Extraoral view. B. Intraoral view.

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