Korean J Gastroenterol.  2018 Apr;71(4):239-243. 10.4166/kjg.2018.71.4.239.

Cronkhite-Canada Syndrome Showing Good Early Response to Steroid Treatment

Affiliations
  • 1Department of Internal Medicine, Dankook University College of Medicine, Cheonan, Korea. nambag1108@gmail.com

Abstract

No abstract available.


MeSH Terms

Intestinal Polyposis*

Figure

  • Fig. 1. Clinical manifestation of the patient at the initial presentation. (A) Hair loss. (B) Skin pigmentation and nail dystrophy. (C) Tongue swelling and mucosal atrophy.

  • Fig. 2. Initial upper and lower endoscopic findings. Numerous variable-sized sessile polyps with mucosal edema and hyperemia were observed in the (A, B) stomach, and (C, D) colon.

  • Fig. 3. Histologic findings. (A) Dilatation of gland, and inflammatory cell infiltration in gastric mucosa (H&E, ×40). (B) Dilatation of gland, cystic dilatation of crypt, and edema of lamina propria in colonic mucosa (H&E, ×40).

  • Fig. 4. Follow-up upper and lower endoscopic findings. Marked regression of polyposis was observed in the (A, B) stomach, and (C, D) colon.

  • Fig. 5. Clinical improvement of the patient at 5 months after steroid administration. Recovery from (A) hair loss and (B) skin pigmentation and nail dystrophy.


Reference

References

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