Anesth Pain Med.
2017 Jul;12(3):240-242. 10.17085/apm.2017.12.3.240.
Anesthetic considerations in a child with Sotos syndrome: A case report
- Affiliations
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- 1Department of Anesthesiology and Pain Medicine, Bundang Jesaeng General Hospital, Seongnam, Korea. tokimga@gmail.com
- KMID: 2388839
- DOI: http://doi.org/10.17085/apm.2017.12.3.240
Abstract
- Sotos syndrome is a rare sporadic genetic disorder characterized by pathognomonic facial features, motor developmental delay induced by hypotonia, learning difficulties, and cardiac and renal anomalies. This report describes the case of a 4-year-old child with Sotos syndrome who underwent a right hydrocelectomy under general anesthesia. We report our experience with airway management, choice of anesthetic drugs, and other anesthetic implications in Sotos syndrome.
MeSH Terms
Reference
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1. Baujat G, Cormier-Daire V. Sotos syndrome. Orphanet J Rare Dis. 2007; 2:36. DOI: 10.1186/1750-1172-2-36. PMID: 17825104. PMCID: PMC2018686.2. Leventopoulos G, Kitsiou-Tzeli S, Kritikos K, Psoni S, Mavrou A, Kanavakis E, et al. A clinical study of Sotos syndrome patients with review of the literature. Pediatr Neurol. 2009; 40:357–64. DOI: 10.1016/j.pediatrneurol.2008.11.013. PMID: 19380072.3. Tatton-Brown K, Rahman N. Sotos syndrome. Eur J Hum Genet. 2007; 15:264–71. DOI: 10.1038/sj.ejhg.5201686. PMID: 16969376.4. Adhami EJ, Cancio-Babu CV. Anaesthesia in a child with Sotos syndrome. Paediatr Anaesth. 2003; 13:835–40. DOI: 10.1046/j.1460-9592.2003.01158.x. PMID: 14617129.5. Chierichini A, Messina A, Vergari A, Santoprete S, Rassanito L. Regional anesthesia in a child with sotos syndrome. Int J Immunopathol Pharmacol. 2011; 24(1 Suppl 2):21–3. DOI: 10.1177/03946320110241S205. PMID: 21669133.6. Varvinski A, McGill FJ, Judd V, Hodzovic I. Sotos’syndrome ellipsis. a rare challenge? Anaesthesia. 2001; 56:809. DOI: 10.1046/j.1365-2044.2001.02181-17.x. PMID: 11493257.7. Jones D, Doughty L, Brown K. Anaesthesia for a child with Sotos’ syndrome. Anaesth Intensive Care. 1991; 19:298–9. PMID: 2069258.8. Raitz R, Laragnoit A. Supernumerary teeth and dental management in Sotos syndrome. J Dent Child (Chic). 2009; 76:246–50.9. McCann ME, Kain ZN. The management of preoperative anxiety in children: an update. Anesth Analg. 2001; 93:98–105. DOI: 10.1097/00000539-200107000-00022. PMID: 11429348.10. Kim JT, Kim HJ, Ahn W, Kim HS, Bahk JH, Lee SC, et al. Head rotation, flexion, and extension alter endotracheal tube position in adults and children. Can J Anaesth. 2009; 56:751–6. DOI: 10.1007/s12630-009-9158-y. PMID: 19639372.11. Suresh D. Posterior spinal fusion in Sotos’ syndrome. Br J Anaesth. 1991; 66:728–32. DOI: 10.1093/bja/66.6.728. PMID: 2064891.12. Sneyd JR, O’Sullivan E. Tracheal intubation without neuromuscular blocking agents: is there any point? Br J Anaesth. 2010; 104:535–7. DOI: 10.1093/bja/aeq060. PMID: 20400611.13. Hung CT, Shih MH, Shih CJ, Liou SC, Kau YC, Chan C, et al. Intubation conditions with low dose rocuronium under sevoflurane induction for children. Chang Gung Med J. 2005; 28:174–9. PMID: 15945324.14. Shi F, Xiao Y, Xiong W, Zhou Q, Yang P, Huang X. Effects of fentanyl on emergence agitation in children under sevoflurane anesthesia: meta-analysis of ran-domized controlled trials. PLoS One. 2015; 10:e0135244. DOI: 10.1371/journal.pone.0135244. PMID: 26275039. PMCID: PMC4537096.15. Wilson W, Taubert KA, Gewitz M, Lockhart PB, Baddour LM, Levison M, et al. Prevention of infective endocarditis: guidelines from the American Heart Association: a guideline from the American Heart Association Rheumatic Fever, Endocarditis, and Kawasaki Disease Committee, Council on Cardiovascular Disease in the Young, and the Council on Clinical Cardiology, Council on Cardiovascular Surgery and Anesthesia, and the Quality of Care and Outcomes Research Interdisciplinary Working Group. Circulation. 2007; 116:1736–54. DOI: 10.1161/CIRCULATIONAHA.106.183095. PMID: 17446442.
