J Korean Assoc Pediatr Surg.  2017 Jun;23(1):5-8. 10.13029/jkaps.2017.23.1.5.

Esophageal Atresia with Bronchogenic Cyst

• Kim Y
• Oh C
• Youn JK
• Han JW
• Kim HY
• Jung SE

• KMID: 2384423
• DOI: http://doi.org/10.13029/jkaps.2017.23.1.5

Abstract

A baby was diagnosed with esophageal atresia (EA) with tracheoesophageal fistula (TEF) on the next day after birth, and end-to-end anastomosis of esophagus with TEF ligation was performed. The distance between proximal and distal esophageal pouch was checked as 3 vertebral body lengths and a 1 cm-sized bronchogenic cyst (BC) was identified near carina on the right side, just below the proximal esophageal pouch. This case report described the baby who have a BC was located between the both esophageal pouch and a longer esophageal gap than usual EA with distal TEF.

Keyword

Esophageal atresia; Tracheoesophageal fistula; Bronchogenic cyst

MeSH Terms

Bronchogenic Cyst*
Esophageal Atresia*
Esophagus
Ligation
Parturition
Tracheoesophageal Fistula

Figure

• 

  Fig. 1 Infantogram shows coiling of the feeding tube, suggesting esophageal atresia (black arrowheads). Patchy opacity in the right lower lung is observed (white arrow).

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  Fig. 2 (A) Operative findings that a bronchogenic cyst (white arrowheads) at the right paratracheal area and distal esophageal fistula (white arrow) were identified. (B) Mimetic diagram of operative findings.

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  Fig. 3 Pathologic findings of cystic mass were consistent with bronchogenic cyst (H&E). (A, B) Histological photographs show fibromuscular walls (A: ×10, B: ×40). (C) The cyst wall is lined by respiratory epithelium (ciliated psuedostratified columnar epithelium) (×100). (D) The cyst wall contains seromucinous bronchial glands (×100).

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