Korean J Ophthalmol.  2016 Jun;30(3):237-239. 10.3341/kjo.2016.30.3.237.

A Rare Case of Acute Ocular Hypertensive Episode in a Patient with Chronic Infantile Neurological Cutaneous Articular Syndrome

• Chan KK
• Ho JC
• Yeung IT
• Ko ST

• KMID: 2373981
• DOI: http://doi.org/10.3341/kjo.2016.30.3.237

Abstract

No abstract available.

MeSH Terms

Chronic Disease
Cryopyrin-Associated Periodic Syndromes/*complications/diagnosis
Gonioscopy
Humans
*Intraocular Pressure
Male
Microscopy, Acoustic
Middle Aged
Ocular Hypertension/diagnosis/*etiology/physiopathology
Rare Diseases

Figure

• 

  Fig. 1 (A) 2004 Fundoscopy showing bilateral blurred optic disc margins, vessel sclerosis, and normal macula. (B) Follow-up after laser iridotomy and argon laser iridoplasty, demonstrating peripheral corneal stromal opacification (red arrows) and anterior chamber activity of the right eye with cells and flare (blue arrows). (C) Ultrasound biomicroscopy of right eye's 9 o'clock position showing invisibility of scleral spur with flat iris configuration (red arrow), no anterior rotation of ciliary body, and incidental finding of small iridociliary cysts (yellow arrows). (D) 2013 Fundoscopy showing similar findings.

Reference

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2. Dollfus H, Hafner R, Hofmann HM, et al. Chronic infantile neurological cutaneous and articular/neonatal onset multisystem inflammatory disease syndrome: ocular manifestations in a recently recognized chronic inflammatory disease of childhood. Arch Ophthalmol. 2000; 118:1386–1392.

3. Terrada C, Neven B, Boddaert N, et al. Ocular modifications in a young girl with cryopyrin-associated periodic syndromes responding to interleukin-1 receptor antagonist anakinra. J Ophthalmic Inflamm Infect. 2011; 1:133–136.

4. Espandar L, Boehlke CS, Kelly MP. First report of keratitis in familial cold autoinflammatory syndrome. Can J Ophthalmol. 2014; 49:304–306.