Ann Dermatol.  2016 Dec;28(6):785-787. 10.5021/ad.2016.28.6.785.

Acquired Dermal Melanocytosis Occurring in a Patient with Hypohidrotic Ectodermal Dysplasia

• Hyun DJ
• Kim DH
• Yoon MS
• Lee HJ

• KMID: 2368139
• DOI: http://doi.org/10.5021/ad.2016.28.6.785

Abstract

No abstract available.

MeSH Terms

Ectodermal Dysplasia 1, Anhidrotic*
Humans

Figure

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  Fig. 1 (A) Multiple bluish patches were observed on the glabella, both cheeks and both temples. Frontal bossing, depressed midface with a saddle nose, and everted lips were also noticed. The patient got a tattoo on the eyebrows for covering absent eyebrows. Periorbital hyperpigmentation over the wrinkled skin was also observed. (B) Hypotrichosis affecting axillary hair. (C) Oligodontia treated with dental prosthesis.

• 

  Fig. 2 Biopsied specimen from the left cheek. (A) Flattened epidermis and hypoplasia of skin appendages was remarkable. Mild superficial perivascular lymphocytic infiltrations were noted (H&E, ×40). (B) Multiple elongated, slightly wavy pigmented cells were seen in the dermis (H&E, ×100; inset: H&E, ×400). The pigmented cells reacted with melan-A (C) and S-100 (D) (×200).

Reference

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