Ann Dermatol.  1993 Jan;5(1):22-24. 10.5021/ad.1993.5.1.22.

A Case of Juvenile Xanthogranuloma Associated with Neurofibromatosis

• Kye YC
• Choi HC
• Oh CH
• Kim SN

• KMID: 2361729
• DOI: http://doi.org/10.5021/ad.1993.5.1.22

Abstract

We report a case of juvenile xanthogranuloma associated with neurofibromatosis. The patient was a 10-month-old female who had multiple yellowish papules on the face and shoulders A Biopsy of these lesions revealed foamy histiocytes with an admixture of inflammatory cells and Touton giant cells. Multiple, more than 6, cafe-au-lait spots, measuring more than 1.5cm in diameter were scattered on the trunk and buttocks Retardation of physical growth and development was observed.

Keyword

Juvenile xanthogranuloma; Neurofibromatosis

MeSH Terms

Biopsy
Buttocks
Cafe-au-Lait Spots
Female
Giant Cells
Growth and Development
Histiocytes
Humans
Infant
Neurofibromatoses*
Shoulder
Xanthogranuloma, Juvenile*