J Korean Soc Coloproctol.  1998 Sep;14(3):621-628.

Gardner's Syndrome Report of one case

Abstract

Gardner's syndrome is a familial disease consisting of gastrointestinal adenomatous polyposis, osteomas of the mandible, skull, and long bones, and a variety of sol tissue lesions, including sebaceous cysts, fibromas, lipomas, and desmoid tumors. The colon is the most common site for polyposis, but the stomach, duodenum, small bowel, and periampullary area may also be involved. The diagnostic evaluation, malignant potential, and management is identical to that for familial adenomatous polyposis. The extracolonic manifestations of Gardner's syndrome are frequent and varied. Gardner's syndrome is inherited as autosomal dominant traits. Authors experienced one case that is a 32 year old female patient who had colonic and duodenal multiple polyposis, desmoid tumor in abdominal wall and right mesocolon and odontoma on mandible.

Keyword

Gardner's syndrome; Desmoid; Odontoma

MeSH Terms

Abdominal Wall
Adenomatous Polyposis Coli
Adult
Colon
Duodenum
Epidermal Cyst
Female
Fibroma
Fibromatosis, Aggressive
Gardner Syndrome*
Humans
Lipoma
Mandible
Mesocolon
Odontoma
Osteoma
Skull
Stomach
Full Text Links
  • JKSC
Actions
Cited
CITED
export Copy
Close
Share
  • Twitter
  • Facebook
Similar articles
Copyright © 2024 by Korean Association of Medical Journal Editors. All rights reserved.     E-mail: koreamed@kamje.or.kr