Yeungnam Univ J Med.  2016 Jun;33(1):44-47. 10.12701/yujm.2016.33.1.44.

Spontaneous renal artery dissection in Ehlers-Danlos syndrome

Affiliations
  • 1Department of Internal Medicine, Wonkwang University School of Medicine, Iksan, Korea. ashneph@wonkwang.ac.kr
  • 2Department of Surgery, Wonkwang University School of Medicine, Iksan, Korea.

Abstract

Primary dissection of the renal artery is rare. Spontaneous renal artery dissection can be associated with diseases such as medial degeneration, neurofibromatosis, syphilitic arteritis, tuberculosis, polyarteritis nodosa, Marfan syndrome, fibromuscular dysplasia, or Ehlers-Danlos syndrome (EDS). Among these causes, EDS related renal artery dissection is very rare worldwide and has not been previously reported in Korea. EDS are a group of heritable connective tissue disorders characterized by fragility of the skin and hypermobility of the joints. We describe the case history of a young man who presented with left side flank pain, hypermobility of the hand joints and showed left renal artery dissection on computed tomography and angiography that turned out to be the first complication of vascular type EDS.

Keyword

Ehlers-Danlos syndrome; Renal artery; Spontaneous dissection

MeSH Terms

Angiography
Arteritis
Connective Tissue
Ehlers-Danlos Syndrome*
Fibromuscular Dysplasia
Flank Pain
Hand Joints
Joints
Korea
Marfan Syndrome
Neurofibromatoses
Polyarteritis Nodosa
Renal Artery*
Skin
Tuberculosis
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