Korean J Dermatol.  2003 Jun;41(6):792-795.

A Case of Atypical Progressive Cribriform and Zosteriform Hyperpigmentation

• Cho SH
• Ha JH
• Choi HC
• Bae EY
• Lee JD

Abstract

We report a case of atypical progressive cribriform and zosteriform hyperpigmentation (PCZH) in a 4-year-old boy. Progressive cribriform and zosteriform hyperpigmentation is a distinctive pigmentary disorder first described by Rower et al. in 1978. It is characterized clinically by uniformly tan cribriform macular pigmentation in a zosteriform distribution and histopathologically by increased melanin in the basal cell layer and absence of nevus cells. This case has two distinctive findings; the onset age was below 10 years and the lesions distributed on the whole body along Blaschko's lines. Histopathologic examination showed pigmentary incontinence.

Keyword

Progressive cribriform and zosteriform hyperpigmentation; Blaschko lines

MeSH Terms

Age of Onset
Child, Preschool
Humans
Hyperpigmentation*
Male
Melanins
Nevus
Pigmentation
Triacetoneamine-N-Oxyl
Melanins
Triacetoneamine-N-Oxyl