Clin Exp Otorhinolaryngol.  2008 Dec;1(4):224-226.

Juvenile Paget's Disease with Paranasal Sinus Aplasia

Affiliations
  • 1Department of Otorhinolaryngology-Head and Neck Surgery, Maryknoll Medical Center, Busan, Korea. entkwon@hanmail.net

Abstract

Juvenile Paget's disease (JPD) is a rare skeletal disorder that's characterized by bone demineralization and elevated levels of serum alkaline phosphatase. JPD involves the paranasal sinuses in extremely rare cases. We report here on a 25-month-old Asian male who was diagnosed of JPD associated with aplasia of the paranasal sinuses, but not the ethmoid sinuses. The patient was successfully treated by surgery and we undertook no medical intervention. This appears to be the first reported case of JPD associated with bilateral paranasal sinus aplasia.

Keyword

Paget disease of bone; Osteitis deformans; Paranasal sinuses; Paranasal sinus neoplasms

MeSH Terms

Alkaline Phosphatase
Asian Continental Ancestry Group
Ethmoid Sinus
Humans
Male
Osteitis Deformans
Paranasal Sinus Neoplasms
Paranasal Sinuses
Preschool Child
Alkaline Phosphatase
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