Korean J Otorhinolaryngol-Head Neck Surg.  2015 May;58(5):330-336. 10.3342/kjorl-hns.2015.58.5.330.

Usefulness of Septodermoplasty in Hereditary Hemorrhagic Telangiectasia

• Yang CJ
• Lee BJ
• Jang YJ

• KMID: 2277862
• DOI: http://doi.org/10.3342/kjorl-hns.2015.58.5.330

Abstract

BACKGROUND AND OBJECTIVES
Epistaxis is the most common symptom in patients with hereditary hemorrhagic telangiectasia (HHT). The aim of this study is to report treatment of severe epistaxis related to HHT with the septodermoplasty and to assess patient outcomes.
SUBJECTS AND METHOD
Six patients with HHT who underwent septodermoplasty from 2009 to 2013 were reviewed retrospectively. We analyzed the clinical characteristics, surgical management and treatment outcomes.
RESULTS
Three patients had been diagnosed with definite HHT and three patients with possible HHT. Three patients had combined abnormal vascular structures in visceral organs. The mean preoperative and postoperative hemoglobin were 7.2 g/dL and 12.8 g/dL, respectively, and visual analogue scale score for frequency and intensity of nasal bleeding remarkably decreased after septodermoplasty in all patients.
CONCLUSION
Septodermoplasty was a safe and efficacious procedure for reducing the frequency and severity of bleeding in most patients with intractable epistaxis and HHT.

Keyword

Epistaxis; Hereditary hemorrhagic telangiectasia

MeSH Terms

Epistaxis
Hemorrhage
Humans
Retrospective Studies
Telangiectasia, Hereditary Hemorrhagic*