Korean J Obstet Gynecol.  2003 Aug;46(8):1604-1609.

A Case of Type II Congenital Cystic Adenomatoid Malformation of the Lung in a Transdiaphragmatic Extralobar Pulmonary Sequestration

• Bae SK
• Kim JY

Abstract

With the current widespread use of obstetric ultrasonography, increasing cases of congenital malformations have been demonstrated antenatally. Both pulmonary sequestration and congenital cystic adenomatoid malformation of the lung (CCAM) are two infrequent congenital pulmonary diseases. The combination of these entities is rare. In the review of literature, this abnormality is so rare that only 80 cases were reported worldwide. To our knowledge, there has been no report that this combined malformation is located transdiaphragmatically. We report the first case of transdiaphragmatic extralobar pulmonary sequestration (ELS) associated with CCAM which was diagnosed by prenatal ultrasonography at 24 weeks gestational age.

Keyword

Extralobar pulmonary sequestration; Congenital cystic adenomatoid malformation

MeSH Terms

Bronchopulmonary Sequestration*
Cystic Adenomatoid Malformation of Lung, Congenital*
Gestational Age
Lung Diseases
Lung*
Ultrasonography
Ultrasonography, Prenatal