Ann Dermatol.  2013 Aug;25(3):352-355. 10.5021/ad.2013.25.3.352.

Touraine-Soulente-Gole Syndrome: A Rare Case Report and Review of the Literature

Affiliations
  • 1Department of Dermatology, G.G.S Medical College and Hospital, Faridkot, India. doc9220@gmail.com

Abstract

Touraine-Soulente-Gole Syndrome (TSG) or pachydermoperiostosis is a rare disorder characterized by pachydermia, periostosis & digital clubbing. Herein, we report a case of a 27 year old male, with the looks of a 47 year old. He presented with excessive wrinkling on his face since past 8 years. TSG syndrome was suspected and examined by histopathological, endocrinological and radiological studies for the confirmation of clinical diagnosis.

Keyword

Hypertrophic osteoarthropathy; Pachydermoperiostosis; Touraine-soulente-gole syndrome

MeSH Terms

Humans
Male
Osteoarthropathy, Primary Hypertrophic

Figure

  • Fig. 1 Cutis verticis gyrata.

  • Fig. 2 Leonine faces.

  • Fig. 3 Broadening of hands and fingers.

  • Fig. 4 Periosteal reaction along the shaft.

  • Fig. 5 Histopathological examination showing hyperplasia epidermal and dermal changes (H&E, ×10).


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