Korean J Med.  2007 Jan;72(1):90-94.

A case of lymphangioleiomyomatosis that presented with recurrent pneumothorax in a postmenopausal woman

Affiliations
  • 1Department of Internal Medicine and Lung Institute, Seoul National University College of Medicine, Seoul, Korea. hansk@snu.ac.kr
  • 2Department of Radiology, Seoul National University College of Medicine, Seoul, Korea.
  • 3Department of Thoracic and Cardiovascular Surgery, Seoul National University College of Medicine, Seoul, Korea.

Abstract

Lymphangioleiomyomatosis is a rare disease which mostly occurs during the reproductive ages of premenopausal women. The presenting symptoms of lymphangioleiomyomatosis include cystic lung lesions, progressive dyspnea on exertion, and recurrent pneumothorax. HRCT shows bilateral diffusely scattered tiny cysts and PFT shows obstructive airflow limitation and decreased diffusion capacity. We report a case of lymphangioleiomyomatosis which presented with recurrent pneumothorax and characteristic cysts in HRCT. The diagnosis was confirmed by pathology. This is the first case of lymphangioleiomyomatosis diagnosed for a postmenopausal woman in Korea. Lymphangioleiomyomatosis must be considered in the diagnosis for a postmenopausal woman with characteristic symptoms and radiologic findings for Korean patients.

Keyword

Lymphangioleiomyomatosis; Menopause; Pneumothorax

MeSH Terms

Diagnosis
Diffusion
Dyspnea
Female
Humans
Korea
Lung
Lymphangioleiomyomatosis*
Menopause
Pathology
Pneumothorax*
Rare Diseases
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