Korean J Gastroenterol.
1997 Apr;29(4):549-553.
Familial Benign Recurrent Intrahepatic Cholestasis
Abstract
- Benign recurrent intrahepatic cholestasis(BRIC) is a very rare cholestatic condition of unknown etiology and its main clinical feature is multiple recurrent episodes of cholestasis with no extrahepatic bile duct obstruction. Familial and nonfamilial forrns of BRIC have been described. We report a case of two sisters with benign recurrent intrahepatic cholestasis. They have experienced recurrent jaundice since childhood. Extrahepatic bile duct obstructions were excluded by ultrasonography and endoscopic retrograde cholangiopancreatography. Liver biopsy specimens showed centri]obular hepatocytic cholestasis. Lobular architectures and portal tracts were well preserved without inflammation.
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