Korean J Anesthesiol.  2009 Sep;57(3):371-375. 10.4097/kjae.2009.57.3.371.

Anesthetic managements for correction of aortic valve regurgitation in a patient with Loeys-Dietz Syndrome: A case report

Affiliations
  • 1Department of Anesthesiology and Pain Medicine, Konkuk University School of Medicine, Seoul, Korea. pondkim@unitel.co.kr

Abstract

Loeys-Dietz Syndrome (LDS) is a recently described autosomal dominant aortic aneurysm syndrome with widespread systemic involvement. It is characterized by the triad of 1) arterial tortuosity and aneurysms, 2) hypertelorism, and 3) bifid uvula or cleft palate. A 12-year-old boy with LDS was scheduled to undergo correction of aortic valve regurgitation due to aortic annuloectasia. We report our clinical experiences of a case of LDS patient with brief review of related literatures and relevant anesthetic problems.

Keyword

Anesthetic managements; Aortic valve regurgitation; Loeys-Dietz Syndrome
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