Korean J Anesthesiol.
2009 Sep;57(3):371-375. 10.4097/kjae.2009.57.3.371.
Anesthetic managements for correction of aortic valve regurgitation in a patient with Loeys-Dietz Syndrome: A case report
- Affiliations
-
- 1Department of Anesthesiology and Pain Medicine, Konkuk University School of Medicine, Seoul, Korea. pondkim@unitel.co.kr
- KMID: 2236511
- DOI: http://doi.org/10.4097/kjae.2009.57.3.371
Abstract
- Loeys-Dietz Syndrome (LDS) is a recently described autosomal dominant aortic aneurysm syndrome with widespread systemic involvement. It is characterized by the triad of 1) arterial tortuosity and aneurysms, 2) hypertelorism, and 3) bifid uvula or cleft palate. A 12-year-old boy with LDS was scheduled to undergo correction of aortic valve regurgitation due to aortic annuloectasia. We report our clinical experiences of a case of LDS patient with brief review of related literatures and relevant anesthetic problems.
- Full Text Links
-
- Actions
-
Cited
- CITED
-
- Close
- Share
-
- Similar articles
-
- Multiple Aortic Operations in Loeys-Dietz Syndrome: Report of 2 Cases
- Valve Sparing Aortic Root Replacement in Children with Loeys-Dietz Syndrome
- Ascending Aortic Rupture in a Young Woman with Loeys-Dietz Syndrome: The First Case Report in Korea
- A Case of Near Total Aortic Replacement in an Adolescent With Loeys-Dietz Syndrome
- Prenatal Diagnosis of an Ascending Aortic Aneurysm Inherited from the Father: A Case Report of Loeys-Dietz Syndrome Type 1
