J Korean Ophthalmol Soc.  2014 Mar;55(3):422-425. 10.3341/jkos.2014.55.3.422.

Pleomorphic Adenoma of the Lacrimal Gland in a Child

• Bae KW
• Kim NJ

• KMID: 2218273
• DOI: http://doi.org/10.3341/jkos.2014.55.3.422

Abstract

PURPOSE
To report one case of pleomorphic adenoma of the lacrimal gland in a child.
CASE SUMMARY
A 7-year-old boy presented with a 2-month history of an exophthalmos and mild ptosis of the left eye; there were no other ophthalmologic problems. Orbit MRI revealed a well-defined mass in the left lacrimal gland and a defect in the orbital roof due to pressure erosion. Tumor resection was performed via a lateral orbitotomy and a biopsy was requested. The biopsy revealed tumor tissue that was composed of epithelial elements with variably sized duct formation. Focal squamous metaplasia and keratin production was also observed.
CONCLUSIONS
Pleomorphic adenoma of the lacrimal gland should be considered as a differential diagnosis of a lacrimal gland mass in a child.

Keyword

Lacrimal gland tumor; Pediatric; Pleomorphic adenoma

MeSH Terms

Adenoma, Pleomorphic*
Biopsy
Child*
Diagnosis, Differential
Exophthalmos
Humans
Lacrimal Apparatus*
Magnetic Resonance Imaging
Male
Metaplasia
Orbit

Figure

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  Figure 1. Pleomorphic adenoma in a 7-year-old boy who had experienced proptosis and upper eyelid ptosis of left eye for 2 months.

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  Figure 2. (A, B) Magnetic resonance imaging of the orbit revealed an encapsulated ovoid mass (arrow) originating from the lacrimal gland and protruding into the orbit.

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  Figure 3. (A) An encapsulated mass 2.1 × 1.2 × 1.2 cm in size was removed. (B) Histopathologic appearance of the tumor showed the myxomatous matrix and cords of epithelial cells. Duct formation is apparent and secreted eosino-philic material (*) is present in the lumen of the duct (H&E, original magnification × 100). (C) Focal area of squamous metaplasia with keratin formation (K) (H&E, original magnification × 200).

Reference

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