J Korean Soc Vasc Surg.  2005 Nov;21(2):151-155.

Vein Ligation Combined with Endovenous Laser Treatment in Klippel-Trenaunay Syndrome: A Case Report

• Chang CY
• Ryu DH
• Jang LC

Abstract

Klippel-Trenaunay syndrome is a rare congenital anomaly combined with capillary, venous malformation and limb hypertrophy, which presents with port-wine stain caused by capillary malformation and varicosities, leg swelling, stasis dermatitis, thrombophlebitis and/or deep vein thrombosis induced by deep vein atresia or hypoplasia, and deep vein obstruction due to fibrous band or persistent marginal vein. Treatment is usually conservative as surgery is technically challenging and the excision of varicose vein is incomplete. However, there are several reports, even when varicosities are recurrent, of clinical improvement following excision of the varicose vein in almost all cases. Here the case of a 12 year-old patient, presenting with severe leg pain due to chronic venous hypertension, treated with vein ligation combined with endovenous laser treatment (EVLT).

Keyword

Klippel-Trenaunay syndrome; Vein ligation

MeSH Terms

Capillaries
Child
Dermatitis
Extremities
Humans
Hypertension
Hypertrophy
Klippel-Trenaunay-Weber Syndrome*
Leg
Ligation*
Port-Wine Stain
Thrombophlebitis
Varicose Veins
Veins*
Venous Thrombosis