J Korean Orthop Assoc.  2011 Jun;46(3):268-272. 10.4055/jkoa.2011.46.3.268.

Coxa Vara with Spondylometaphyseal Dysplasia

• Kim TS
• Kim SH
• Chung KS

• KMID: 2185471
• DOI: http://doi.org/10.4055/jkoa.2011.46.3.268

Abstract

Developmental coxa vara is a rare disease and the symptoms do not appear at birth, but rather, they appear at the age of walking. Clinically, the symptoms include a waddling gait, limb length discrepancy and frequent weariness. Developmental coxa vara is sometimes associated with skeletal dysplasia. Especially, it is associated with spondylometaphyseal dysplsia and the vertebral bodies and long bones are affected. The authors report here on diagnosing and treating this rare disease and we review the relevant literatures.

Keyword

coxa vara; spondylometaphyseal dysplasia; corner fracture

MeSH Terms

Coxa Vara
Extremities
Gait
Hip
Osteochondrodysplasias
Parturition
Rare Diseases
Walking
Osteochondrodysplasias

Figure

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  Figure 1 (A) A radiograph shows coxa vara with decreased neck-shaft angle and increased Hilgenreiner-epiphyseal angle (H-E angle). (B) A radio graph shows spondylometaphyseal dysplasia characterized with platyspondyly. (C) There is a marked sclerosis, flaring of the metaphyseal end of distal tibia and fibula. (D) Irregular areas of metaphyses also present corner fracture on medial aspect of proximal tibia.

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  Figure 2 Anteroposterior radiograph after subtrochanteric valgus osteotomy.

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  Figure 3 Anteroposterior radiograph taken 2 years after subtrochanteric valgus osteotomy shows the recurrence of developmental coxa vara on the right hip.

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  Figure 4 Anteroposterior radiograph after revision subtrochanteric valgus osteotomy due to recurrence of coxa vara.

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  Figure 5 This radiograph shows the decreased Hilgenreiner-epiphyseal angle 3 years after revision subtrochanteric valgus osteotomy.

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