J Cardiovasc Ultrasound.  2012 Dec;20(4):193-196. 10.4250/jcu.2012.20.4.193.

Porcelain Heart: Rapid Progression of Cardiac Calcification in a Patient with Hemodialysis

• Lee HU
• Youn HJ
• Shim BJ
• Lee SJ
• Park MY
• Jeong JU
• Gu GM
• Jeon HK
• Lee JE
• Kwon BJ

• KMID: 2177407
• DOI: http://doi.org/10.4250/jcu.2012.20.4.193

Abstract

Cardiac calcification usually occurs in patients with end-stage renal disease. However, rapid progression of cardiac calcification is rarely associated with secondary hyperparathyroidism of end-stage renal disease. We report a patient with end-stage renal disease who showed moderate left ventricular hypertrophy at the first echocardiography, and showed severe myocardial calcification and severe mitral valve stenosis 4 years later. We suspected a rapid progression 'porcelain heart' cardiomyopathy secondary to hyperparathyroidism of end-stage renal disease. The patient underwent parathyroidectomy, and considered mitral valve replacement.

Keyword

End stage renal disease; Secondary hyperparathyroidism; Myocardial calcification; Mitral valve stenosis

MeSH Terms

Cardiomyopathies
Dental Porcelain
Echocardiography
Humans
Hyperparathyroidism
Hyperparathyroidism, Secondary
Hypertrophy, Left Ventricular
Kidney Failure, Chronic
Mitral Valve
Mitral Valve Stenosis
Parathyroidectomy
Renal Dialysis
Dental Porcelain

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