Ann Dermatol.  2011 Oct;23(Suppl 2):S243-S246. 10.5021/ad.2011.23.S2.S243.

Multiple Unilateral Zosteriform Connective Tissue Nevi on the Trunk

• Choi YJ
• Lee SJ
• Choi CW
• Kim WS
• Lee GY

• KMID: 2156800
• DOI: http://doi.org/10.5021/ad.2011.23.S2.S243

Abstract

Connective tissue nevus is not a true tumor, but rather a hamartoma involving various components of connective tissue. It presents as a slow-growing, painless, flesh-colored, or pink nodule or plaque that is evident from childhood. While any region of the body may be affected, there is a predilection for the trunk and extremities. A 20-month-old girl presented with three ipsilateral confluent popular plaques with zosteriform distribution that had formed over the previous 17 months on the left chest and abdomen. The patient remained asymptomatic. Unlike all previously reported cases demonstrating a single lesion, we report a connective tissue nevi in a child who presented with multiple unilateral zosteriform lesions, an unusual pattern of distribution without evidence of tuberous sclerosis complex.

Keyword

Connective tissue nevus; Tuberous sclerosis complex; Zosteriform

MeSH Terms

Abdomen
Child
Connective Tissue
Extremities
Hamartoma
Humans
Infant
Nevus
Thorax
Tuberous Sclerosis
Nevus

Figure

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  Fig. 1 (A) Two (C4, T1~3) ipsilateral segmental erythematous to flesh-colored plaques with numerous confluent papules and several discrete dome-shaped papules (arrow) on the left anterior chest. (B) The third (T11~12) segmental lesion on the abdomen.

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  Fig. 2 (A) Widespread presence of thick collagen bundles in the dermis (H&E, ×40). (B) Abundant dense collagen fibers in the dermis (Masson-Trichrome, ×40). (C) Decreased elastic tissue in the dermis (Elastic, ×40).

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