Ann Dermatol.  2011 May;23(2):222-224. 10.5021/ad.2011.23.2.222.

Linear Lichen Sclerosus along the Blaschko's Line of the Face

• Kim CR
• Jung KD
• Kim H
• Jung M
• Byun JY
• Lee DY
• Lee JH
• Yang JM
• Lee ES

• KMID: 2156668
• DOI: http://doi.org/10.5021/ad.2011.23.2.222

Abstract

Lichen sclerosus et atrophicus (LSA) is an inflammatory disease that primarily causes anogenital lesion in middle aged women. We present here a case of facial LSA with an asymptomatic, well-demarcated, whitish to bluish, atrophic patch in a linear pattern on the forehead of a 48-year-old woman. This case showed an atypical clinical presentation and it mimicked en coup de sabre, but the histopathologic results confirmed the diagnosis of LSA.

Keyword

Blaschko's line; Extragenital; Lichen sclerosus; Linear scleroderma; Morphea

MeSH Terms

Female
Forehead
Humans
Lichen Sclerosus et Atrophicus
Lichens
Middle Aged
Scleroderma, Localized

Figure

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  Fig. 1 A linear, well-demarcated atrophic patch on the forehead (black arrow).

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  Fig. 2 (A) Thinning of the epidermis, loss of the rete ridges, focal basal cell vacuolization, pigmentary incontinence, edema and hyalination of the papillary dermis along with a moderate lymphomononuclear cell infiltrate are noted (H&E stain, ×100). (B) Special staining for elastic fiber showed scanty elastic tissue in the dermis (Elastic fiber, ×100).

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