Ann Dermatol.  2007 Mar;19(1):38-42. 10.5021/ad.2007.19.1.38.

Three Cases of Congenital Smooth Muscle Hamartomas

Affiliations
  • 1Department of Dermatology, Kangbuk Samsung Hospital, School of Medicine, Sungkyunkwan University, Seoul, Korea. chaptainkim@hanmail.net
  • 2Department of Dermatology, Cheil General Hospital, School of Medicine, Sungkyunkwan University, Seoul, Korea.

Abstract

Congenital smooth muscle hamartomas (CSMHs) usually appear at birth as skin-colored or slightly hyperpigmented patches or plaques on the trunk or extremities and are often covered by and increased amount of vellus hair. Histopathologically, it represents a proliferation of smooth muscle bundles within the dermis(1,2). We herein report on three cases of localized CSMHs; Case 1 was a 2-month-old boy who presented with a skin-colored, 6x5cm-sized plaque with folds, hypertrichosis and pseudo- Darier's sign on the face, an unusual site. But there was no hyperpigmentation. Case 2 and 3 were both 1-month-old boys who presented with typical hyperpigmented, hairy plaques on the lateral aspect of the left thigh.

Keyword

Congenital smooth muscle hamartoma; Hypertrichosis; Pseudo-Darier's sign

MeSH Terms

Extremities
Hair
Hamartoma*
Humans
Hyperpigmentation
Hypertrichosis
Infant
Infant, Newborn
Male
Muscle, Smooth*
Parturition
Thigh
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