J Korean Med Sci.  2010 Jun;25(6):950-952. 10.3346/jkms.2010.25.6.950.

An Infrarenal Aortic Hypoplasia Presented with Claudication

• Sung SA
• Hwang YH
• Lee SY
• Cho YK
• Kwon TW

• KMID: 2150878
• DOI: http://doi.org/10.3346/jkms.2010.25.6.950

Abstract

We describe a case of infrarenal aortic hypoplasia in a 52-yr-old woman who presented with claudication. Computed tomographic angiography revealed an abrupt absence of the infrarenal aorta, with collateral flow reconstituting the iliofemoral systems. After a polytetrafluoroethylene graft was interposed between the aortic stump and the iliac bifurcation, the patient's claudication resolved.

Keyword

Aortic Coarctation; Intermittent Claudication

Figure

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  Fig. 1 Computed tomographic angiography showed an abrupt segmental occlusion of infrarenal aorta (white arrows). Both renal arteries were intact. The proximal and distal abdominal aorta were reconstituted by multiple collaterals, such as marginal artery of Drummond, the anastomosis between superior mesenteric and inferior mesenteric artery, bilateral epigastric, lumbar, and abdominal superficial arteries.

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  Fig. 2 Operative findings revealed absence of infrarenal aorta replaced with fibrous band (white arrows). Inferior mesenteric artery (black arrow) reconstituted the abdominal aortic system.

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  Fig. 3 The microscopic image showed fibromyxoid degeneration (H&E stain; magnification×100, ×400 in small box).

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  Fig. 4 Computed tomographic angiography showed a patent graft between thoracoabdominal junction to aortic bifurcation (arrows).

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