J Korean Ophthalmol Soc.  2015 Jul;56(7):1141-1148. 10.3341/jkos.2015.56.7.1141.

Three Cases of Outer Retinal Tubulation in Bietti's Crystalline Dystrophy

Affiliations
  • 1Cheil Eye Hospital, Daegu, Korea. ppjinsun25@hanmail.net
  • 2Department of Ophthalmology, Kyungpook National University School of Medicine, Daegu, Korea.

Abstract

PURPOSE
To report the prevalence and the characteristics of outer retinal tubulation (ORT) in Bietti's crystalline dystrophy in 6 eyes of 3 patients. CASE SUMMARY: Three patients with Bietti's crystalline dystrophy were examined using color fundus photography, fundus autofluorescence picture, spectral domain optical coherence tomography (SD-OCT), fluorescein angiography, electroretinogram and electrooculogram. ORT was detected in 3 of 3 (100%) Bietti's crystalline dystrophy patients. SD-OCT B-scan revealed hyperreflective material inside the hyporeflective internal space with hyperreflective border. ORT was observed under the fovea or outside the fovea and on the outer nuclear layer in the retina. ORTs were no greater than 70 x 140 microm in size when measured using SD-OCT B-scan image.
CONCLUSIONS
ORT was observed frequently in patients with Bietti's crystalline dystrophy. These findings can potentially predict the extensive photoreceptor abnormalities in retinal pigment epithelial atrophy.

Keyword

Bietti's crystalline dystrophy; Outer retinal tubulation; Spectral domain optical coherence tomography
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