Ann Rehabil Med.  2015 Oct;39(5):833-837. 10.5535/arm.2015.39.5.833.

Multiple Lower Extremity Mononeuropathies by Segmental Schwannomatosis: A Case Report

Affiliations
  • 1Department of Rehabilitation Medicine, College of Medicine, The Catholic University of Korea, Seoul, Korea. yjko@catholic.ac.kr

Abstract

Schwannoma is an encapsulated nerve sheath tumor that is distinct from neurofibromatosis. It is defined as the occurrence of multiple schwannomas without any bilateral vestibular schwannomas. A 46-year-old man with multiple schwannomas involving peripheral nerves of the ipsilateral lower extremity presented with neurologic symptoms. Electrodiagnostic studies revealed multiple mononeuropathies involving the left sciatic, common peroneal, tibial, femoral and superior gluteal nerves. Histologic findings confirmed the diagnosis of schwannoma. We reported this rare case of segmental schwannomatosis that presented with neurologic symptoms including motor weakness, which was confirmed as multiple mononeuropathies by electrodiagnostic studies.

Keyword

Schwannomatosis; Mononeuropathies; Electromyography

MeSH Terms

Diagnosis
Electromyography
Humans
Lower Extremity*
Middle Aged
Mononeuropathies*
Neurilemmoma
Neurofibromatoses
Neurologic Manifestations
Neuroma, Acoustic
Peripheral Nerves

Figure

  • Fig. 1 (A) Initial sagittal T1-weighted image shows tumor inside medial hamstring muscle (arrow). (B) T2-weighted image demonstrates hyperintense lesions along the course of the sciatic nerve.

  • Fig. 2 (A) Sagittal T2-weighted image shows multiple hyperintense tumors along the course of the tibial nerve. (B) Proximal lesion has a similar appearance with a bright signal.

  • Fig. 3 (A) Axial T2-weighted image demonstrates the well-circumscribed lesions along the course of the tibial nerve. (B) Distal lesions are well-circumscribed and extend into the soleus muscle.


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