J Korean Ophthalmol Soc.  1998 Aug;39(8):1823-1830.

Retinal Vascular Changes and Treatment of incontinentia Pigmenti Eyes

Affiliations
  • 1Department of Ophthalmology, College of Medicine, Seoul National University.
  • 2Department of Dermatology, College of Medicine, Seoul National University.

Abstract

The retinal vascular changes and the results of treatment were studied in five incontinentia pigmenti patients. All patients were female and had a mean follow-up of 4 1/2 years (7 months~7 1/2 years). Abnormal retinal vascular changes included peripheral avascular retina, retinal and preretinal neovascularization, and dilated, tortuous retinal vessels. Two of them were treated; one received a cryotherapy and the other a laser photocoagulation to the avascular retinal area and showed regression of abnormal vessels. At last follow-up, no eye developed retinal detachment, but traction of the peripheral retina by a vitreous band was visible in three patients. One showed a degenerative macula and an atrophy of the retinal pigment epithelium in the papillomacular bundle area. Our result suggests that incontinentia pigmenti eyes may show retinal vascular changes very similar to that in retinopathy of prematurity, and can be effectively treated by destroying an avascualr retina if indicated.

Keyword

Avascular retina; Cryotherapy; Incontinentia pigmenti; Laser photocoagulation; Neovascularization

MeSH Terms

Atrophy
Cryotherapy
Female
Follow-Up Studies
Humans
Incontinentia Pigmenti*
Light Coagulation
Retina
Retinal Detachment
Retinal Pigment Epithelium
Retinal Vessels
Retinaldehyde*
Retinopathy of Prematurity
Traction
Retinaldehyde
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