J Korean Soc Radiol.
2010 Sep;63(3):249-253. 10.3348/jksr.2010.63.3.249.
Monolobar Caroli's Disease in Left Lobe of the Liver: A Case Report
- Affiliations
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- 1Department of Radiology, Wonkwang University Hospital, Korea. yjyh@wonkwang.ac.kr
- KMID: 2097901
- DOI: http://doi.org/10.3348/jksr.2010.63.3.249
Abstract
- Caroli's disease is a rare congenital hepatobiliary disease characterized by multifocal segmental dilatation of the intrahepatic bile ducts and hepatic fibrosis that can cause bile duct stones, cholangitis, and cholangiocarcinoma. The disease may diffusely affect the liver or be localized to one lobe or segment. Less than 20% of all reported cases of Caroli's disease are the monolobar type. We report a case of Caroli's disease of the monolobar type, which was confined to segment 4a of the liver in a 30-year-old man. The disease was diagnosed by CT and Gd-EOB-DTPA enhanced MRI, and confirmed histopathologically after a hepatic lobectomy.
