J Korean Pediatr Soc.
2000 Oct;43(10):1386-1389.
A Case of Omphalocele-Exstrophy-Imperforate Anus-Spinal Defects(OEIS syndrome)
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- 1Department of Pediatrics, College of Medicine, Soonchunhyang University, Chunan, Korea.
Abstract
- Omphalocele-exstrophy-imperforate anus-spinal defects(OEIS Syndrome) is a single defect in early mesoderm, and its incidence is about one in 250,000. If was first described by Littre in 1709. The characteristics of this disorder is omphalocele, extrpohy of bladder, imperforate anus and spina bifida. There have been reports of longtime survival made possible by several operations, but for most cases normal life is impossible due to the deformities. We report a case of OEIS complex who had omphalocele, exstrophy of bladder, imperforate anus and spina bifida from birth.
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