Korean J Leg Med.  2003 May;27(1):101-105.

Arrhythmogenic Right Ventricular Dysplasia/Cardiomyopathy: Report of an Autopsy Case

Affiliations
  • 1National Institute of Scientific Investigation, Korea. isyme@nisi.go.kr

Abstract

Arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C) is characterized histologically by massive infilteration of right ventricular wall by fat tissue with surviving strands of cardiomyocytes bordered by or embedded in fibrosis. ARVC has been recognized as a cause of sudden death, especially in the young. We report an autopy case of ARVD/C in a 35-year-old female. She was found dead in her house under apparently natural circumstances. The autopsy revealed a dilated 340-gram heart with a fibrofatty replacement of the right ventricular myocardium. On the review of her past medical history, she had taken medical examination for prolonged general weakness about 1 year prior to death. At that time the echocardiogram revealed dilatation of right ventricular cavity size and moderately decreased left ventricular systolic function, the electrocardiogram revealed R>S at V1 lead and T-wave inversion at V1-V3 leads. To the best of our knowledge, this is the second autopsy case of ARVD/C, reported in the literature of Korea.

Keyword

Right ventricular dysplasia/cardiomyopathy; Arrhythmogenic cardiomyopathy; Sudden death

MeSH Terms

Adult
Autopsy*
Death, Sudden
Dilatation
Electrocardiography
Female
Fibrosis
Heart
Humans
Korea
Myocardium
Myocytes, Cardiac
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