Korean J Med.  2004 Nov;67(Suppl 3):S732-S735.

A case of relapsing polychondritis with vasculitis mimicking Takayasu's arteritis

Affiliations
  • 1Department of Internal Medicine, College of Medicine, Seoul National University, Seoul, Korea. ysong@snu.ac.kr

Abstract

Relapsing polychondritis is a rare autoimmune disease of unknown etiology characterized by recurrent inflammation of cartilaginous structures of the ears, nose, respiratory tract and joints. Relapsing polychondritis may affect proteoglycan-rich tissues, such as the eyes, aorta, heart, and skin. Several cardiovascular complications have been reported in patients with relapsing polychondritis. The most common findings of cardiovascular manifestations are aortic or mitral regurgitation and aortic aneurysm. Aortitis is a very rare complication of relapsing polychondritis. We report a case of 48-year-old man who had relapsing polychondritis with aortitis mimicking Takayasu's arteritis.

Keyword

Relapsing polychondritis; Aortitis; Takayasu's arteritis

MeSH Terms

Aorta
Aortic Aneurysm
Aortitis
Autoimmune Diseases
Ear
Heart
Humans
Inflammation
Joints
Middle Aged
Mitral Valve Insufficiency
Nose
Polychondritis, Relapsing*
Respiratory System
Skin
Takayasu Arteritis*
Vasculitis*
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