Anesth Pain Med.  2010 Oct;5(4):329-332.

General anesthesia for a spinal muscular atrophy type I patientundergoing feeding gastrostomy: A case report

Affiliations
  • 1Department of Anesthesiology and Pain Medicine, Paik Hospital, College of Medicine, Inje University, Busan, Korea. maeteo@hanmir.com

Abstract

Spinal muscular atrophy (SMA) in children leads to progressive muscle weakness, dysphagia, aspiration, and death. The most common and severe form of SMA is designated as type I, also known as Werdnig-Hoffman Disease or Floppy Baby syndrome. We anesthetized an 8 month-old female infant with SMA type I undergoing feeding gastrostomy. We planned to use inhalational anesthesia without muscle relaxants. Anesthesia and surgery were uneventful. We herein report a case of successful peri-operative anesthetic management for SMA type I infant with aspiration pneumonia.

Keyword

Gastrostomy; Neuromuscular disease; Spinal muscular atrophy type I

MeSH Terms

Anesthesia
Anesthesia, General
Child
Deglutition Disorders
Female
Gastrostomy
Humans
Infant
Muscle Weakness
Muscles
Muscular Atrophy, Spinal
Neuromuscular Diseases
Pneumonia, Aspiration
Spinal Muscular Atrophies of Childhood
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