Korean J Dermatol.  2014 Nov;52(11):817-820.

A Case of Systematized Inflammatory Linear Verrucous Epidermal Nevus with Mandibular Hypoplasia

• Kim HS
• Ha JM
• Cho EB
• Park EJ
• Kim KH
• Kim KJ

Abstract

Inflammatory linear verrucous epidermal nevus (ILVEN) is an uncommon variant of verrucous epidermal nevus, clinically characterized by erythematous and hyperkeratotic verrucous papules with a typical linear arrangement. Most reported cases present as solitary lesions, but systematized ILVEN is rare. Epidermal nevus syndrome is a congenital disorder in which epidermal nevi are associated with abnormalities in other organ systems. However, ILVEN has been reported rarely in association with such abnormalities, including those of the skeleton. Here we report a rare case of systematized ILVEN presenting with concomitant mandibular hypoplasia.

Keyword

Inflammatory linear verrucous epidermal nevus; ILVEN; Mandibular hypoplasia

MeSH Terms

Congenital, Hereditary, and Neonatal Diseases and Abnormalities
Nevus
Nevus, Sebaceous of Jadassohn*
Skeleton