Korean J Urol.  1973 Sep;14(3):239-244.

A Case of Adrenogenital Syndrome

Affiliations
  • 1Department of Urology, School of Medicine, Chonnam National University, Korea.

Abstract

The adrenogenital syndrome owing to congenital adrenal hyperplasia is an inborn error of adreno-cortical metabolism, as a result of excessive adrenal androgens. producing heterosexual virlizing changes in females and isosexual precocity in males. Here, a case of adrenogenital syndrome developed in 14 year-old Korean female was presented. She had an enlarged clitoris and vaginal introitus communicated to the urethra interior to the urethral meatal opening at the perineum, resembling perineal hypospadiac penis. Exploration of the pelvic cavity and left adrenal gland revealed normal female internal genital organs and hyperplastic adrenal gland. Constructive operation including vaginoplasty and clitoridectomy was performed.

Keyword

adrenogenital syndrome

MeSH Terms

Adolescent
Adrenal Glands
Adrenal Hyperplasia, Congenital
Adrenogenital Syndrome*
Androgens
Circumcision, Female
Clitoris
Female
Genitalia
Heterosexuality
Humans
Male
Metabolism
Penis
Perineum
Urethra
Androgens
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