J Korean Soc Radiol.  2011 Jul;65(1):81-83. 10.3348/jksr.2011.65.1.81.

Gastrointestinal Stromal Tumor of the Appendix Mimicking a Mucinous Cystadenocarcinoma: A Case Report

• Lee MH
• Lee HK
• Yi BH
• Kim HK

• KMID: 1443497
• DOI: http://doi.org/10.3348/jksr.2011.65.1.81

Abstract

A gastrointestinal stromal tumor of the appendix is a rare entity. Only a few cases have been reported in this location to date. We present here a case of a pathologically confirmed gastrointestinal stromal tumor of the appendix mimicking a mucinous cystadenocarcinoma in a 67-year-old man.

MeSH Terms

Aged
Appendix
Cystadenocarcinoma, Mucinous
Gastrointestinal Stromal Tumors
Humans
Mucins
Mucins

Figure

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  Fig. 1 A. Pre-contrast axial CT image shows a cystic mass with internal soft-tissue component in the right lower quadrant abdominal cavity, which appeared to abut to the cecum in the other CT images. Note the wall calcification (arrows). B, C. Post-contrast axial (B) and coronal (C) CT images show the same cystic mass with irregular, enhancing wall thickening. The internal soft-tissue component (arrowhead) enhances heterogeneously. Note the tubular structure (arrow) abutting the mass, which was connected with the mass in other CT images, representing that the mass arises from the appendix.

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  Fig. 2 The cut surface of the surgical specimen shows a tan-white mass with extensive areas of hemorrhage and cystic degeneration (arrows).

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  Fig. 3 Photomicrograph of histopathologic specimen shows that the tumor cells are strongly reactive for C-Kit in immunohistochemical stain (× 200).

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