Korean J Radiol.  2004 Dec;5(4):287-290. 10.3348/kjr.2004.5.4.287.

Unilocular Extrahepatic Biliary Cystadenoma Mimicking Choledochal Cyst: A Case Report

• Park JH
• Lee DH
• Kim HJ
• Ko YT
• Lim JW
• Yang MH

• KMID: 1118837
• DOI: http://doi.org/10.3348/kjr.2004.5.4.287

Abstract

We report here on a case of extrahepatic biliary cystadenoma arising from the common hepatic duct. A 42-year-old woman was evaluated by us to find the cause of her jaundice. Ultrasonography and CT showed a cystic dilatation of the common hepatic duct and also marked dilatation of the intrahepatic duct. Direct cholangiography demonstrated a large filling defect between the left hepatic duct and the common hepatic duct; dilatation of the intrahepatic duct was also demonstrated. Following excision of the cystic mass, it was pathologically confirmed as a unilocular biliary mucinous cystadenoma arising from the common hepatic duct.

Keyword

Bile ducts, extrahepatic; Cyst, choledochal cyst; Cyst, unilocular

MeSH Terms

Adult
Bile Duct Neoplasms/*diagnosis
Cholangiopancreatography, Magnetic Resonance
Choledochal Cyst/*diagnosis
Cystadenoma/*diagnosis
Diagnosis, Differential
Female
Hepatic Duct, Common/*pathology/radiography/ultrasonography
Humans
Tomography, X-Ray Computed
Ultrasonography, Interventional

Figure

• 

  Fig. 1 Unilocular extrahepatic biliary cystadenoma in a 42-year-old woman. A, B. Abdominal CT scans show marked dilatation of the intrahepatic duct and the cystic dilatation of the common bile duct (arrow). C. Ultrasonography also shows cystic dilatation of the extrahepatic duct. On retrospective review, the thin partial septum like structure (arrow) is seen at the upper aspect of the cystic dilatation of the extrahepatic duct. D. Endoscopic retrograde cholangiopancreatography shows a well-demarcated large filling defect (arrow) in the common hepatic duct with dilatation of the intrahepatic duct. It does not communicate with the bile duct. The PTBD tube, which is not filled with contrast material, is also seen in the left hepatic duct. E. Magnetic resonance cholangiopancreatography clearly shows the thin wall (arrow) of the cystic lesion in the common hepatic duct. It also shows a bile duct variation; the right posterior segmental duct drained into the left hepatic duct. F. The surgical specimen shows a unilocular cystic mass arising from the common hepatic duct (incised). GB; gallbladder G. Microscopically (H & E staining, ×200), the cyst wall is lined by a single layer of columnar mucin-secreting cells (arrows). The epithelium is supported by ovarian-like stroma.

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