Korean J Ophthalmol.  2011 Oct;25(5):352-354. 10.3341/kjo.2011.25.5.352.

Unilateral Peters' Anomaly with Chorioretinal Coloboma in the Other Eye

• Cho D
• Choi D
• Nam W

• KMID: 1098640
• DOI: http://doi.org/10.3341/kjo.2011.25.5.352

Abstract

An 18-year-old man presented with poor vision in both eyes that had been present since birth. Central corneal opacity and inferior peripheral sclerocornea with iridocorneal adhesion were observed upon anterior segment examination of the left eye. A coloboma of the iris was observed in the patient's right eye, which manifested as a small notch in the inferior pupillary margin and cataract. Fundus examination of the right eye showed a large inferior chorioretinal coloboma involving the optic disc and macula. It is essential to examine the fundus in detail, if possible, in cases of Peters' anomaly, because these patients may have congenital anomalies such as chorioretinal coloboma.

Keyword

Chorioretinal coloboma; Peters'anomaly; Retinal detachment

MeSH Terms

*Abnormalities, Multiple
Adolescent
Anterior Eye Segment/abnormalities
Choroid/*abnormalities
Coloboma/*diagnosis
Corneal Opacity/*diagnosis
Diagnosis, Differential
Eye Abnormalities/*diagnosis
Humans
Male
Microscopy, Acoustic
Optic Nerve/abnormalities
Retina/*abnormalities

Figure

• 

  Fig. 1 Central cornea. opacity and inferior peripheral sclerocornea with iridocorneal adhesion in the left eye.

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  Fig. 2 Inferior iris coloboma with cataract in the right eye.

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  Fig. 3 Large chorioretinal coloboma affecting the retina and optic nerve head in the right eye.

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  Fig. 4 (A) Vertical axial scan of the right eye shows staphyloma. (B) Vertical axial scan of the left eye shows normal findings.

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