J Korean Ophthalmol Soc.  1999 Jun;40(6):1727-1731.

A Case of Benign Nonte ratoid Medulloepithelioma of the Optic Nerve Head

Affiliations
  • 1Department of Ophthalmology, College of Medicine, Chung-ang University.

Abstract

Medulloepithelioma(diktyoma) is a uncommon congenital tumor that is generally believed to arise from the embryonic neuroepithelium of the medullary tube. This tumor usually arises from the ciliary body epithelium. But medulloepitheliomas of the retina and optic nerve may also occur, although it is extremely rare, because the embryonal medullary epithelium that lines the optic vesicle is continuous with the epithelium lining the cavity of the optic nerve during the early embryonal period. The occurrence of medulloepithelioma of the optic nerve is exceptionally rare, with only a few cases have been previously reported. We report a first case of medulloep-ithelioma of the optic nerve head in Korea in a 5-year-old girl who presented with a poor vision and squint of the left eye.

Keyword

Medulloepithelioma; Optic nerve head

MeSH Terms

Child, Preschool
Ciliary Body
Epithelium
Female
Humans
Korea
Neuroectodermal Tumors, Primitive*
Optic Disk*
Optic Nerve*
Retina
Strabismus
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