Korean J Med.  2000 Feb;58(2):234-239.

A case of systemic lymphangiomatosis with splenic involvement

Affiliations
  • 1Department of Internal Medicine, College of Medicine, Institute of Digestive Diseases and Nutrition, Korea Universitiy, Seoul, Korea.

Abstract

Lymphangiomatosis is a very rare and slow-growing benign tumor generally accepted to be the result of a congenital malformation of the lymphatic system. It is most commonly found in the neck, axilla and less commonly retroperitoneum, mediastinum, mesentery, omentum, pelvis, bone, skin, scrotum, and spleen. We present a patient who had systemic lymphangiomatosis with splenic involvement. She was presented with the cystic neck mass suspected to be a cystic hygroma during the first decade. She complained of the mass on left upper quadrant of abdomen at the age of 28. Under full investigations, we had diagnosed the lymphangiomatosis involving spleen and right adrenal gland, and splenectomy was done. We present a case of systemic lymphangiomatosis with emphasis on diagnosis, management, and prognosis.

Keyword

Spleen; Lymphangiomatosis

MeSH Terms

Abdomen
Adrenal Glands
Axilla
Diagnosis
Humans
Lymphangioma, Cystic
Lymphatic System
Mediastinum
Mesentery
Neck
Omentum
Pelvis
Prognosis
Scrotum
Skin
Spleen
Splenectomy
Full Text Links
  • KJM
Actions
Cited
CITED
export Copy
Close
Share
  • Twitter
  • Facebook
Similar articles
Copyright © 2024 by Korean Association of Medical Journal Editors. All rights reserved.     E-mail: koreamed@kamje.or.kr