J Korean Radiol Soc.  1998 Mar;38(3):519-522. 10.3348/jkrs.1998.38.3.519.

Uterine Didelphys with Blind Hemivagina, Hematocolpos, Ipsilateral Renal Agenesis (UD-BHRA) and BilateralOvarian Tumors: A Case Report

• Lee YR
• Choi BI
• Park HW
• Kook SH

• KMID: 2201413
• DOI: http://doi.org/10.3348/jkrs.1998.38.3.519

Abstract

Uterine didelphys is a congenital malformation characterized by the presence of two separated hemiuteri andhemivaginas, due to lack of midfusion of the Mullerian ducts. We report a case of UD-BHRA(uterine didelphys withblind hemivagina and ipsilateral renal agenesis), a rare type of uterine didelphys charaterized by symptomaticunilateral hematocolpos due to blind hemivagina after menarche and ipsilateral renal agenesis. The MRI findings in22-year-old woman with bilateral ovarian tumors demonstrated two separated uterine horns and cervical and vaginalcanals, with left hematocolpos and left renal agenesis.

Keyword

Uterus, MR; Uterus, abnormalities; Ovary, neoplasms

MeSH Terms

Animals
Female
Hematocolpos*
Horns
Humans
Magnetic Resonance Imaging
Menarche
Mullerian Ducts

Figure

• 

  Fig. 1. A case of uterine didelphys with blind hemivagina and ipsilateral renal agenesis in 22-year-old female. A. SE Tl weighted (TR/TE=600/h) axial scan shows left renal agenesis. B. FSE T2 weighted (TR/TE=3000/85) axial scan shows two separated uterine cavities with normal signal intensities of the endometrium and the junctional zones(arrows). C. FSE T2 weighted (TR/TE=4000/85) sagittal image shows high signal intensity of paravaginal mass representing hematocolpos (arrows) and the right ovarian tumor (arrowheads) proved as yolk sac tumor mixed with teratoma. D SE Tl weighted (TR/TE=600/ll) axial scan shows intermediate signal intensitiy of right ovarian mass (arrows) and high signal intensity of left ovarian mass (arrow heads) proved as mature teratoma. E- F. FSE T2 weighted (TR/TE=3000/85) axial images peroformed after operation clearly demonstrated two separated uterocervical canals (arrows on Fig. E)and hemivaginas (arrows on Fig. F) without communication.

Reference

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