J Korean Med Sci.  2006 Feb;21(1):169-171. 10.3346/jkms.2006.21.1.169.

Congenital Atrophoderma of Pasini and Pierini

• Kim SK
• Rhee SH
• Kim YC
• Lee ES
• Kang HY

• KMID: 2157803
• DOI: http://doi.org/10.3346/jkms.2006.21.1.169

Abstract

Idiopathic atrophoderma of Pasini and Pierini is a form of dermal atrophy of unknown etiology, usually affecting women during their adolescence and young adulthood. A 2-yr-old girl was presented with erythematous atrophic lesion on the right shoulder, which appeared from birth. The histologic findings were consistent with atrophoderma. This patient, to the best of our knowledge, is the first case of atrophoderma with an onset since birth.

Keyword

Atrophy; Dermis; congenital

MeSH Terms

Atrophy/congenital/metabolism
Biopsy
Child, Preschool
Collagen/metabolism
Erythema/pathology
Female
Humans
Skin/*pathology

Figure

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  Fig. 1 Atrophic erythematous plaques on the right shoulder.

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  Fig. 2 The involved skin (A) showed markedly reduced dermal thickness when compared with adjacent normal skin (B); hematoxylin-eosin stain, ×40. The collagen bundles in the dermis of the lesion are slightly homogenized in appearance (C); hematoxylin-eosin stain, ×400.

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