J Korean Foot Ankle Soc.  2015 Dec;19(4):193-196. 10.14193/jkfas.2015.19.4.193.

Melorheostosis with Synovial Chondromatosis of the Foot: A Report of Two Cases

• Lee CC
• Kim SW
• Choi HJ
• Hwang IY
• Kim MS

• KMID: 2132464
• DOI: http://doi.org/10.14193/jkfas.2015.19.4.193

Abstract

Melorheostosis is a rare disease, belonging to the sclerotic bone dysplasia group. Initially described by Leri and Joanny in 1922, its etiology remains unknown. Onset is usually insidious, with deformity of the extremity, pain, limb stiffness, and limitation of motion in the joints. The typical radiographic appearance consists of irregular hyperostotic changes of the cortex, resembling melted wax dripping down one side of a candle. Treatment is usually symptomatic and conservative; however, conservative treatment is unsatisfactory due to functional issues when involving the distal extremity. We report on two cases of melorheostosis with synovial chondromatosis of the foot treated by mass excision.

Keyword

Melorheostosis; Synovial chondromatosis; Ankle; Foot

MeSH Terms

Ankle
Bone Diseases, Developmental
Chondromatosis, Synovial*
Congenital Abnormalities
Extremities
Foot*
Joints
Melorheostosis*
Rare Diseases

Figure

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  Figure 1. Preoperative anteroposterior plain radiography shows several sclerotic changes in the fourth metatarsal bone and irregular flowing hyperostosis along fourth metatarsal bone.

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  Figure 2. An axial T2-weighted magnetic resonance image of melorheostosis patient shows low signal intensity juxtacortical nodular lesion in the dorsal aspect of the fourth metatarsal bone.

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  Figure 3. The dorsal surface of the bony mass was exposed during operation.

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  Figure 4. Postoperative anteroposterior plain radiography shows complete excision of irregular flowing hyperostosis.

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  Figure 5. A photomicrograph shows melorheostosis and synovial chondromatosis (H&E stain, ×40).

Reference

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