J Korean Neurosurg Soc.  1981 Mar;10(1):341-346.

Histiocytosis X Case Report

• Choi CS
• Park KS
• Park KY
• Ju MB

Abstract

Eosinophilic granuloma, Hand-Schuller-Christian and Abt-Letterer-Siewe syndrome are known to be the same disease entity involving the reticulohistiocytic system of the body, although their clinical manifestations are different. So they were included under the term of Histiocytosis X and this concept has been generally accepted. The authors have experienced one case of Hand-Schuller-Christian disease and that of eosinophilic granuloma. The former was a 23 years old man with complaints of exophthalmos, polyuria and a tender palpable mass on the right parietal area and in the latter a soft pulastile mase located on the left parietal area in a 3 year old boy. There was no neurological deficits on their admission. We managed them with radiation and steroid therapy following surgical curettage.

MeSH Terms

Child, Preschool
Curettage
Eosinophilic Granuloma
Exophthalmos
Histiocytosis*
Histiocytosis, Langerhans-Cell*
Humans
Male
Polyuria
Rabeprazole
Young Adult