Korean J Thorac Cardiovasc Surg.  2002 Mar;35(3):239-243.

Budd-Chiari Syndrome Due to Antithrombin,Protein C and Protein S Deficiency and the Complete Obstruction of SVC

• Kim TY
• Lee WY
• Hong KW
• Kim EJ
• Shin YC
• Kim KI
• Rhim CY
• Ryu KH
• Choi YJ

Abstract

In this case, a 39 year-old man was admitted with Budd-Chiari syndrome associated with complete superior vena cava(SVC)obstruction causing general edema and hepatic failure. Conservative medical therapy was failed. And after the radiologist failed to invasive procedure of balloon dilatation, we attempted the inferior vena cava to right atrium bypass graft. Operation was done through median sternotomy and extended vertical oblique abdominal incision. A 24 mm Dacron tube was placed from the inferior vena cava just below the left renal vein to the right atrium without using the cardiopulmonary bypass pump. The patient's postoperative course was uneventful without signs of bleeding or anyother complications. We used anticoagulants at the postoperative first day. At the postoperative 26th day, we performed abdominal Doppler sonography and we confirmed that the graft patency was good. The patient was discharged with SVC obstructive symptoms but we noticed relief of SVC obstructive symptoms in the course of follow-up.

Keyword

Budd-Chiari syndrome; Vena cava, superior; Superior vena cava syndrome

MeSH Terms

Adult
Anticoagulants
Budd-Chiari Syndrome*
Cardiopulmonary Bypass
Dilatation
Edema
Follow-Up Studies
Heart Atria
Hemorrhage
Humans
Liver Failure
Polyethylene Terephthalates
Protein S Deficiency*
Protein S*
Renal Veins
Sternotomy
Superior Vena Cava Syndrome
Transplants
Vena Cava, Inferior
Vena Cava, Superior
Anticoagulants
Polyethylene Terephthalates
Protein S