Yonsei Med J.  2005 Oct;46(5):715-718. 10.3349/ymj.2005.46.5.715.

Recurrent Retroperitoneal Cystic Lymphangioma

• Ozdemir H
• Kocakoc E
• Bozgeyik Z
• Cobanoglu

• KMID: 2158155
• DOI: http://doi.org/10.3349/ymj.2005.46.5.715

Abstract

Retroperitoneal cystic lymphangioma is a rare congenital malformation. The majority of lymphangiomas are present at birth and nearly all present before the age of two years. We report a case of giant cystic retroperitoneal lymphangioma in a patient who first presented with symptoms at the age of 7, underwent surgery, and who then suffered a recurrent mass 11 years later.

Keyword

Lymphangioma; retroperitoneal; ultrasonography; computed tomography; magnetic resonance imaging

MeSH Terms

Tomography, X-Ray Computed
Retroperitoneal Neoplasms/*diagnosis/pathology/surgery
Recurrence
Male
Magnetic Resonance Imaging
Lymphangioma, Cystic/*diagnosis/pathology/surgery
Humans
Adolescent

Figure

• 

  Fig. 1 Transverse sonogram of the left flank demonstrating a large mass with multiloculated, thick septum and having hyperechogenic calcific foci (arrow).

• 

  Fig. 2 Transaxial abdominal CT scan demonstrating low attenuation cysts of the retroperitoneum displacing the pancreas (arrow) anteriorly and mildly compressing the adrenal and left kidney. Calcification is seen as high attenuation foci in the cyst.

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  Fig. 3 A. Axial T2 weighted MR (TR 3000 ms, TE 112 ms) and B. Coronal T2 weighted MR showing a high signal intensity mass lesion in the retroperitoneum.

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  Fig. 4 Pathologic specimen showing multiple cystic spaces containing lymphoid and endothelial cells (hematoxylineosin ×100).

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