- A Case of Porphyria with reversible MRI findings
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Kang SY, Ma HI, Kwak KH, Lee SA
- KMID: 2342655
- J Korean Neurol Assoc.
- 1998 Apr;16(2):241-244.
The porphyrias are inherited or acquired disorders of specific enzymes in the heme biosynthetic pathway. Porphyrias have diverse neurologic manifestations with unknown mechanism. Some authors have proposed ischemic vasculopathy... -
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- Severe neurologic manifestations in acute intermittent porphyria developed after spine surgery under general anesthesia: a case report
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Park EY, Kim YS, Lim KJ, Lee HK, Lee SK, Choi H, Kang MH
- KMID: 1966759
- Korean J Anesthesiol.
- 2014 Sep;67(3):217-220.
- doi: 10.4097/kjae.2014.67.3.217
Porphyrias are inherited metabolic disorders resulting from a specific enzyme defect in the heme biosynthetic pathway. Porphyrias are induced by various precipitants. Clinical features include abdominal pain, neurologic manifestations, autonomic... -
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- A Case of Erythorpoietic Porphyria
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Suh EO, Ihm CW
- KMID: 1678329
- Korean J Dermatol.
- 1981 Oct;19(5):733-740.
No abstract available. -
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- A Case of Acute Hepatic Porphyria
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Han YC, Joo SH, Kang JH, Lee BC
- KMID: 1682547
- J Korean Pediatr Soc.
- 1988 Feb;31(2):253-257.
No abstract available. -
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- A case report of anesthesia management in the liver transplantation recipient with porphyria: A case report
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Song HW, Shin YH, Ko JS, Gwak MS, Kim GS
- KMID: 2236457
- Korean J Anesthesiol.
- 2012 Jan;62(1):83-86.
- doi: 10.4097/kjae.2012.62.1.83
Porphyrias are a group of diseases characterized by an enzyme deficiency in the heme biosynthesis pathway, resulting in accumulation of precursor molecules in the tissue. Some porphyric patients develop progressive... -
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- A Case of Pseudoporphyria
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Um SH, Oh CW
- KMID: 2302682
- Korean J Dermatol.
- 2005 Mar;43(3):394-397.
Pseudoporphyria is a generic term that is used to describe photoaggravated bullous dermatoses associated with multiple iatrogenic causes, including medications and dialysis. The bullous lesions of pseudoporphyria are similar to... -
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- Acute Intermittent Porphyria Presenting with Periodic Leg Pain
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Lee HJ, Kim S, Oh J
- KMID: 2370973
- J Korean Neurol Assoc.
- 2017 Feb;35(1):53-54.
- doi: 10.17340/jkna.2017.1.14
No abstract available. -
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- A Case of Secondary Porphyrinopathy Induced by Chronic Alcoholism
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Lim HJ, Kim HS, Kim HO, Park YM
- KMID: 2248032
- Korean J Dermatol.
- 2008 Nov;46(11):1534-1537.
The disturbance of porphyrin metabolism is principally differentiated into the porphyrias and secondary porphyrinopathies. Alcohol, drugs, heavy metal, and various diseases can cause secondary porphyrinopathy. Among them, alcohol is a... -
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- A Case of Porphyria with Acute Pancreatitis
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Chung SW, Han JH, Ju YM, Yoon KH, Yang WS, Lee SK, Hong SK, hAN EM, Kim BS, Lee KU
- KMID: 1540031
- J Korean Soc Endocrinol.
- 2000 Mar;15(1):128-132.
The porphyrias are a group of disorders caused by deficiency in the enzymes of the heme biosynthetic pathway. Patients with porphyria may develop neurovisceral attacks which include severe abdominal pain,... -
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- Porphyria cutanea tarda precipitated by alcohol abuse
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Kim HY, Kim JH, Lee SH, Son HY
- KMID: 2256338
- Korean J Med.
- 2007 Dec;73(6):670-671.
No abstract available. -
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- Liver Cirrhosis Induced by Porphyria Cutanea Tarda: A Case Report and Review
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Lee KG, Hyun JJ, Seo YS, Keum B, Yim HJ, Jeen YT, Lee HS, Chun HJ, Kim CD, Ryu HS, Um SH
- KMID: 2167266
- Gut Liver.
- 2010 Dec;4(4):551-555.
Porphyria cutanea tarda (PCT) is a metabolic disorder that results in a decrease in uroporphyrinogen decarboxylase activity. It is characterized by photosensitivity, bullae formation, and skin pigmentation. There are four... -
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- Porphyria Cutanea Tarda in a Hemodialysis Patient
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Suh KS, Han SH, Kim JH, Lee KH, Park JB, Kim ST, Jang MS
- KMID: 2245838
- Korean J Dermatol.
- 2016 Jan;54(1):81-83.
No abstract available. -
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- Inborn Errors of Metabolism in Korea
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Lee HJ
- KMID: 2185707
- J Korean Neurol Assoc.
- 2004 Feb;22(1):1-10.
Diseases of inborn errors of metabolism (IEMs) are very rare but the overall prevalence of IEMs is not low, and in the United States, about 5~10% of admitted patients have... -
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- Sporadic Porphyria Cutanea Tarda in a Patient with Multiple Sclerosis Treated with Interferon Beta 1-a Therapy: A Case Report
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Carrieri P, Petracca M, Montella S, Cerullo G, Cerillo I, Cimmino G
- KMID: 2287559
- J Clin Neurol.
- 2013 Jul;9(3):196-197.
- doi: 10.3988/jcn.2013.9.3.196
No abstract available. -
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- Four Cases of Porphyria Cutanea Tarda
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Kim SH, Chung SL, Kim SW
- KMID: 1678744
- Korean J Dermatol.
- 1983 Aug;21(4):421-427.
Porphyria cutanea tarda(PCT) is a photocutaneous disorder due to excessive porphyrins in the skin. We experienced 4 male patients who showed typical clinical manifestations. Histologic findings revealed subepidermal bullae with... -
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- Porphytia Cutanea Tarda: Report of a Case
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Kim ST, Seong HS, Chung TA
- KMID: 1664432
- Korean J Dermatol.
- 1974 Sep;12(3):183-186.
A case of porphyria cutanca tarda is reported, in which the photosensitive cutaneous symptoms developed in association with impaired hepatic function possibly related to chronic consumption of alcohol. Wood's light... -
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- Acute Intermittent Porphyria and Pregnancy
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Ryu JH, Choi EA, Choi HM, Kim TY, Cho JS, Park YW, Kim JW
- KMID: 1924482
- Korean J Obstet Gynecol.
- 1997 Feb;40(2):414-418.
The Porphyria are a group of inherited and acquired disorders characterized by partial defects in the heme biosynthetic pathway. Among the hepatic forms, acute intermittent porphyria(AIP) is the most severe... -
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- A Case of Congenital Erythropoietic Porphyria
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Hwang JS, Na GY, Chung SL, Suh SB
- KMID: 2231645
- Korean J Dermatol.
- 1985 Oct;23(5):686-690.
A 3-year-old-male had the appearance of red urine at birth and developed recurrent bullae in sun-exposed area of the skin, erythrodontia, alopecia, splenomegaly and hemolytic anemia, We observed coral red... -
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- Ocular Manifestations of Pediatric Systemic Disease
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Lim HW, Oh SY
- KMID: 2350369
- Hanyang Med Rev.
- 2016 Aug;36(3):182-185.
- doi: 10.7599/hmr.2016.36.3.182
Pediatric diseases are important because diagnosis and care for these can be complex. Among them, specific diseases have been associated with ocular involvement. This review presents the ocular manifestations of... -
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- Severe Bradycardia and Hypotension during Spinal Anesthesia in a Patient with Agent Orange Sequela: A case report
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Yun CS, Lee JH, Lee JY, Lee KN, Moon JI
- KMID: 2032433
- Korean J Anesthesiol.
- 1998 Mar;34(3):650-654.
- doi: 10.4097/kjae.1998.34.3.650
Various defoliant herbicides were sprayed to kill vegetation and thereby denied cover to enemy forces in Vietnam war, and the defoliant was later alleged to have caused long-lasting health problems... -
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